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38 Neonatal and Infant M tality 2020 | NMH Annual Rep t Perinatal Mortality: Congenital Anomalies – Livebirths (11) Case No. EGA BW (g) Gender Delivery method Apgars (1, 5, 10 mins) Age at death (days) Place of death External Referral IUGR Placental Histology Cause of death PM 1 22+2 910 Male SVD Not recorded 1 Delivery Ward No No SUA. Lymphocytic deciduitis. Congenital high airway obstruction syndrome (CHAOS), renal agenesis. No 2 34+2 2650 Male LSCS 1, 2, 2 3 Paediatric hospital Yes No High grade FVM. Hypercoiled cord. Right sided congenital diaphragmatic hernia with hydrops, multi organ failure, deep white matter brain injury. No 3 34+3 3350 Male LSCS 8, 7 1 Theatre Yes No Normal. Severe congenital brain abnormalities; hydrocephalus and lissencephaly and associated arthrogryphosis caused by mutation in L1CAM gene – 'MASA syndrome' . Yes 4 34+5 2725 Male LSCS 2, 3, 3 1 NICU Yes No Low grade FVM Hydrops fetalis, congenital chylothorax, no genetic cause identified on whole exome sequence. No 5 35+2 2020 Female SVD 6, 6 1 Delivery Ward No No Gross only. Multiple congenital anomalies, Smith Lemli Opitz syndrome (DHCR7 gene mutation) . No 6 36+1 2855 Male LSCS 2, 2 1 Theatre Yes No Low grade FVM. Pulmonary hypoplasia, anhydramnios, megacystis and renal dysplasia. No 7 37+2 3685 Male LSCS 6, 9 3 NICU No No Gross only. Severe tricuspid valve dysplasia, tricuspid regurgitation and pulmonary atresia. No 8 37+6 3025 Male LSCS Not recorded 1 Theatre No No Gross only. Left congenital diaphragmatic hernia, 8p23 deletion. No 9 38+5 2410 Female LSCS 4, 6, 6 1 Theatre Yes No Normal. Hypoplastic left heart syndrome, intact atrial septum, aortic stenosis, mitral atresia, hypoplastic aortic arch. No 10 39+1 3995 Male LSCS 3, 1, 1 1 Theatre No No High grade FVM. Delayed villous maturation. Complex congenital heart disease – tricuspid valves dysplasia, severe tricuspid regurgitation, trisomy 21, hydrops fetalis. No 11 41+4 2370 Male SVD 1, 0 1 Delivery Ward No Suspected antenatally Gross only. Trisomy 18. No Neonatal & Infant M tality